Search results for " Burgundy"

showing 10 items of 10 documents

Expanding the Phenotype Associated with NAA10-Related N-Terminal Acetylation Deficiency

2016

International audience; N-terminal acetylation is a common protein modification in eukaryotes associated with numerous cellular processes. Inherited mutations in NAA10, encoding the catalytic subunit of the major N-terminal acetylation complex NatA have been associated with diverse, syndromic X-linked recessive disorders, whereas de novo missense mutations have been reported in one male and one female individual with severe intellectual disability but otherwise unspecific phenotypes. Thus, the full genetic and clinical spectrum of NAA10 deficiency is yet to be delineated. We identified three different novel and one known missense mutation in NAA10, de novo in 11 females, and due to maternal…

0301 basic medicineMaleModels MolecularMicrocephalyMutation MissenseBiologyGermlineKEY WORDS: NAA1003 medical and health sciencesGermline mutationGenes X-LinkedIntellectual disabilityGeneticsmedicineMissense mutationHumansGenetic Predisposition to DiseaseN-Terminal Acetyltransferase EGenetics (clinical)Genetic Association StudiesGerm-Line MutationN-Terminal Acetyltransferase AResearch ArticlesGeneticsX-linked[SDV.GEN]Life Sciences [q-bio]/GeneticsRegional Council of BurgundyMosaicismN-terminal acetylationAcetylationmedicine.diseasePhenotypePedigreeOgden SyndromeX‐linked030104 developmental biologyNAA10intellectual disabilityN‐terminal acetylationContract grant sponsors: Dijon University HospitalFemale[ SDV.GEN ] Life Sciences [q-bio]/GeneticsNAA15Research ArticleHuman Mutation
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Proposer des révisions intersessions aux étudiants de 1ère année : quelles relations avec la réussite aux examens ?

2013

This paper assesses a revision programme proposed to unsuccessful students between the two examination sessions within the framework of the "Plan réussite en Licence" in first year at the University of Burgundy, both in terms of student participation and links with achievement. The low participation of students is not associated with particular student profiles. An analysis of the students' future shows that student participation in the revision programme led to a lower drop-out risk during the second examination session and greater success, but only as regards the examinations of the 2nd semester. It should also be noted that student participation also has positive effects in the mid-term …

Dispositif d'aideRéussite universitaire[SHS.EDU]Humanities and Social Sciences/Education[SHS.EDU] Humanities and Social Sciences/EducationEducational measuresRéussiteExamination sessionsEducationDispositif d'accompagnementFlunking0502 economics and businessDevelopmental and Educational PsychologyÉtudiant de 1ère annéeAbandonEffetAide aux étudiants4. EducationPersévérance05 social sciences050301 educationRevisions[ SHS.EDU ] Humanities and Social Sciences/EducationExamenUniversity of BurgundyStudent achievementUniversitéProgramme d'étudesFreshmen0503 education050203 business & managementRévisionUniversité de Bourgogne
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Representación y delegación de poderes. Los usos públicos del mandato en el ducado de Borgoña (siglos XIII-XIV)

2019

El presente trabajo trata sobre los usos públicos dados a la técnica romano-canónica del mandato en el ducado de Borgoña durante el siglo XIII y principios del XIV. El artículo tiene como objetivo mostrar la centralidad de esta técnica en las prácticas de delegación de facultades y de representación, esenciales para el ejercicio del gobierno laico en el Occidente medieval. 

History[SHS.ARCHEO] Humanities and Social Sciences/Archaeology and Prehistory[SHS.ARCHEO]Humanities and Social Sciences/Archaeology and PrehistoryDelegationCorporate governancemedia_common.quotation_subjectPoder; justicia; Gobernanza; institucionesHistoriaRepresentation (politics)Attorneyship; Delegation of Powers; Mandate; Duchy of Burgundy; Capeto governmentPoliticsProcuración; Delegación de Poderes; Mandato; Ducado de Borgoña; Gobierno capetoPolitical scienceDuchyHumanitiesComputingMilieux_MISCELLANEOUSmedia_commonAnos 90
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Les rois de France et l’affirmation de l’autorité ducale durant le principat de Robert II de Bourgogne (1272-1306)

2018

The reign of Robert II of Burgundy (1272-1306) marks a rupture within the Capetian duchy'sgovernment. The evolutions that feature his governance are deeply linked to the relations that unitehim to the kings contemporary to his reign such as Philip III the Bold and Philip IV the Fair.Showing signs of a flawless faithfulness, Robert II places himself close to these kings in order toreaffirm his authority and to fulfill his own ambitions. This rapprochement is due to two majorevents - the first one being the matrimonial policy initiated by the Dukes of Burgundy since HughIV and the second one the numerous favours from Robert II to the kings both in the military fieldand regarding royal gov…

XIIIe siècle[ SHS.HIST ] Humanities and Social Sciences/HistoryRobert II de Bourgogne[SHS.HIST] Humanities and Social Sciences/HistoryDukes of BurgundyGovernmentGouvernementPouvoirsPowersThirteenth century[SHS.HIST]Humanities and Social Sciences/HistoryRois de FranceDuché de Bourgogne
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Le cimetière du second Âge du fer de la Tournière à Lailly (Yonne) : nouvelle analyse des fouilles anciennes

2021

International audience; Cette étude présente de manière critique les découvertes qui ont été faites à la fin du xix e siècle et au début du xx e siècle à Lailly La Tournerie (Yonne). Elle propose un classement typologique et chronologique de tous les objets mis au jour par catégorie fonctionnelle, ainsi que la reconstitution, pour la première fois, de plusieurs ensembles clos. Elle a ainsi permis de proposer une évolution de ce cimetière entre le second quart du v e siècle (La Tène A ancienne) et la première décennie du ii e siècle avant J.-C. (La Tène C1). L'analyse des pratiques funéraires a également été abordée à l'aide d'un dépouillement systématique des rares données existantes. Leur …

[SHS.ARCHEO]Humanities and Social Sciences/Archaeology and Prehistorypratiques funérairesmortuary practicesalte SammlungSecond Iron AgeYonneLa TèneKörpergrabcemeteryMetallfundeglassLatèneinhumationold collection. Schlagwörter Bourgogne[SHS.ARCHEO] Humanities and Social Sciences/Archaeology and Prehistorycimetièremetal artifactsBestattungssittenmobilier métalliqueverrecollection ancienne BurgundyGlasNekropoleMots-clés Bourgognejüngere Eisenzeitsecond âge du Fer
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Pierres et carrières : réflexions autour de différentes stratégies d’approvisionnement sur les chantiers bourguignons médiévaux

2021

In this paper, we want to discuss the complexity of the mechanisms of medieval building stone supplying based on a diachronically and multidisciplinary inquiry on several Cistercian and ducal study cases. The first results enlighten the constraint caused by land property that limits the builders to a supplying network shaped by domain and law. Thanks to the growing vitality of trade and the arrival of independent stone providers, criteria of selection gradually focus on stone itself. Both global and individual strategies evolve then, reinventing the networks of stone providing and the markets.

[SHS.ARCHI]Humanities and Social Sciences/Architecture space management[SHS.ARCHEO] Humanities and Social Sciences/Archaeology and Prehistorystratégie d'approvisionnementsupply strategy[SHS.ARCHEO]Humanities and Social Sciences/Archaeology and Prehistorymatériaux de constructionrecyclagerecyclingquarrycistercianscraftsmanduke of Burgundycistercienbuilding materials[SHS.HIST] Humanities and Social Sciences/Historyduc de Bourgogneartisan[SHS.ARCHI] Humanities and Social Sciences/Architecture space management[SHS.HIST]Humanities and Social Sciences/Historycarrière
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Justifier les dépenses vestimentaires dans la recette générale de toutes les finances du duc de Bourgogne Philippe le Bon

2014

La série comptable de la recette générale de toutes les finances sous le duc de Bourgogne Philippe le Bon, remarquablement bien conservée, permet une approche fine et précise de la conjoncture vestimentaire de l’hôtel ducal, mais aussi, dans une large mesure, de l’évolution de la comptabilité. Les outils de contrôle importants, à tous les niveaux, mais aussi les changements de personnel et les réformes régulières témoignent des difficultés de l’autorité ducale à maîtriser ses finances. Le compte, outil de travail personnel, évolue en fonction de la personnalité du receveur et des contraintes auxquelles il est soumis. Ces contraintes se renforcent à l’orée des années 1440, dans un contexte g…

comptabilitéaccountsMoyen Âge[ SHS.HIST ] Humanities and Social Sciences/HistoryGarderobeausgaben.reforma de la haciendaBuchhaltungPhilippe le Bon (1419-1467)duque de Borgoñafinancial reformHistoireVêtementclothes expendituresContabilidadFinanzreformenFelipe el Buenocompra de ropa[SHS.HIST] Humanities and Social Sciences/Historyduc of Burgundy Philipp the Good (regn 1419-1467)duc de Bourgogne Phillipe le Bon (règne 1419-1467)réforme des finances[SHS.HIST]Humanities and Social Sciences/HistoryComputingMilieux_MISCELLANEOUSdépenses vestimentaires
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Costume and vestimentary device at the court of Philipp III of Burgundy from 1430 to 1455

2003

This study of vestimentary device at the court of burgundy from 1430 to 1455 leans on the systematic and computed analysis of the duke Philipp III of Burgundy's accounting. It turns towards five points : describing the terminology of costume and its written speech ; bringing nearer the vestimentary production and court activities, year by year, in relation with chroniclers accounts ; understanding the organisation of supplies based on humans reports (organisational chart, life of a garment, purveyors' tables) ; analysing rythms and levels of consummation, one by one, or in groups , with, in particular, a point about dress right at this time ; understanding the vestimentary personality of th…

duc de Bourgogne dit le Bonaccounts<br />Comptabilitéeconomy of clothCostume Textileapearence culturesaid the goodCourt lifeVie de cour Economie domestique [SHS]Humanities and Social SciencesDressVêtementclothingPhilipp III duke of burgundyCulture des apparences[ SHS ] Humanities and Social SciencesPhilippe III[SHS] Humanities and Social Sciences
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Histoire naturelle des oiseaux.

Science Ornithology Burgundy
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Conclusiones ex universa philosophia depromptae… [Placard de thèse (1639) imprimé sur soie].

DIJON university Burgundy
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